Relapsing organising pneumonitis in a man with primary biliary cirrhosis, CREST syndrome, and chronic pancreatitis.

We report a relapsing, steroid-responsive, organising pneumonitis, in a man with the CREST syndrome (calcinosis, Raynaud's phenomenon, oesophageal dysfunction, sclerodactyly, and telangiectasia) variant of systemic sclerosis and primary biliary cirrhosis. This pattern of pulmonary disease has not previously been described in systemic sclerosis. The association between primary biliary cirrhosis and the CREST syndrome is well recognised in women' and we report the association in a man.